眼窩的胞狀軟部肉瘤

Alveolar Soft Part Sarcoma of the Orbit

10.30048/ACTASOS.198705.0108

吳俊昇(Juin-Sen Wu)；高淑卿(Shu-Ching Kao)；林嘉理(Chia-Lee Lin)；劉榮宏(Jorn-Hon Liu)；向扶（白丰）(Fu-Gau Shiang)

alveolar soft part sarcoma ； orbit

台灣眼科醫學會會刊

26卷2期（1987 / 05 / 01）

603 - 607

繁體中文

本篇報告一位十七歲的年輕男性病患，左側眼窩部位突出一巨大腫瘤已有六年，且有右半邊肢體運動障礙及感覺喪失。電腦斷層攝影和X光片顯示腫瘤已轉移至腦部及肺部。手術前，經由動脈血管攝影將左側內顎動脈栓塞，減少手術當中之出血。局部切除後，病理報告證實為－胞狀軟部肉瘤。

This case was a 17-year-old patient with a huge mass protruding from left orbit for 6 years. On neurological examination, right hemiparesis and sensory loss of right side to pin prick, position sense and cortical sensation were noted. CT scan of brain showed a tumor mass chiefly arising from left orbit with calcification, involving left maxillary sinus and extending intracranially through the left side of skull base to the left side of lateral ventricle, causing hydrocephalus. Chest PA X-ray showed multiple metastasis. Selective internal maxillary and common carotid angiogram was performed by femoral catheterization and followed by Ivolon powder for embolization of internal maxillary artery to reduce the tumor size and prevent massive bleeding during operation. After simple excision, the specimen was sent to pathologist and reported as alveolar soft part sarcoma which showed organoid epithelial-like nests or alveolar arrangement of their cell components separated by thin trabeculae containing capillary. The cells are large, polygonal with small to median sized darkly staining nuclei, and abundant cytoplasm rich in acidophilic granules that were PAS-positive and diastase resistant. Also, some calcifications were noted. 5 months later, this patient expired due to respiratory failure.