题名

Isolated IgG4-Related Sclerosing Cholangitis Mimicking Cholangiocarcinoma: A Case Report

并列篇名

像膽管癌的單獨IgG4相關性硬化性膽管炎-病例報告

作者

陳昆忠(Kun-Zhong Chen);柯萬盛(Wang-Sheng Ko)

关键词

IgG4 ; IgG4-related sclerosing cholangitis ; lgG4 ; IgG4相關性硬化性膽管炎

期刊名称

醫學與健康期刊

卷期/出版年月

7卷1期(2018 / 03 / 01)

页次

105 - 111

内容语文

英文

中文摘要

An 82-year-old man was admitted for intermittent upper abdominal pain that had lasted for one month. Abdominal Computed Tomography and Magnetic Resonance Cholangiopancreatography revealed dilated bilateral intrahepatic bile ducts and a mass-like lesion at the bifurcation of intrahepatic ducts. Klatskin tumor was highly suspected and surgical treatment was performed. Pathological report revealed common bile duct with abundant IgG4-positive plasma cells and lymph nodes with reactive lymphoid hyperplasia. Subsequently, serum IgG4 level found to be substantially increased, leading to a diagnosis of IgG4-related sclerosing cholangitis (IgG4-SC). Because malignant tumors are frequently suspected on initial presentation, clinicians should differentiate malignant tumors from IgG4-SC, because IgG4-SC responds well to steroid therapy.

英文摘要

一名82歲男性因間歇性上腹痛一個月而住院,腹部電腦斷層及膽道磁振造影檢查顯示肝内膽管擴大,並在肝内膽管分叉處有一個疑似腫瘤,當時高度懷疑Klatskin腫瘤,並進行手術治療。病理報告顯示膽總管具有豐富的IgG4陽性漿細胞,及淋巴結具有反應性淋巴樣增生,同時血清IgG4濃度升高,確定診斷為IgG4相關性硬化性膽管炎。此疾病對類固醇治療反應良好及初始常懷疑膽管惡性腫瘤,所以IeG4相關性硬化性膽管炎應該考慮予以鑑別診斷。

主题分类 醫藥衛生 > 預防保健與衛生學
醫藥衛生 > 社會醫學
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