胸腔病例（三三一）肺部動靜脈畸形

10.6666/ClinMed.2016.78.5.024

莊凡毅；陳威志

肺動靜脈畸形(pulmonary arteriovenous malformation, PAVM) ； 遺傳性出血性血管擴張症(hereditary hemorrhagic telangiectasia, HHT) ； Osler-Weber-Rendu syndrome ； 胸前顯影劑增強心臟超音波(transthoracic contrast echocardiography, TTCE) ； 血管攝影栓塞(embolization)

臨床醫學月刊

78卷5期（2016 / 11 / 25）

294 - 298

繁體中文

肺動靜脈畸形(pulmonary arteriovenous malformation, PAVM) 乃指肺部動脈及靜脈間異常的連接。在一般族群中不常見，但在出現低血氧、肺部結節或咳血等症狀之患者則需列入鑑別診斷。肺動靜脈畸形可為遺傳性出血性血管擴張症(hereditary hemorrhagic telangiectasia, HHT 或稱Osler-Weber-Rendu syndrome) 的一種表現。本文介紹一位確診(definite) 遺傳性出血性血管擴張症合併肺動靜脈畸形的男性病例，接受血管栓塞術後症狀明顯改善，並針對肺動靜脈畸形以及遺傳性出血性血管擴張症做一簡單介紹。

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