题名

偉大的模仿者：IgG4相關性疾病

DOI

10.6666/ClinMed.201902_83(2).0014

作者

劉志偉；蔡長祐

关键词

IgG4相關性疾病（IgG4 related disease） ； 自體免疫胰臟炎（autoimmune pancreatitis） ； 纖維化（fibrosis）

期刊名称

臨床醫學月刊

卷期/出版年月

83卷2期（2019 / 02 / 22）

页次

75 - 80

内容语文

繁體中文
中文摘要

IgG4相關性疾病是這十年來一種新的多重器官影響、多重系統性表現的疾病，此疾病常見特徵為IgG4血清濃度大於135mg/dl、受侵犯組織有大量IgG4陽性漿細胞浸潤、席紋樣纖維化（storiform fibrosis）、閉塞性靜脈炎（obliterative phlebitis）。診斷主要由臨床表現以及組織切片的病理結果。治療主要是使用皮質性類固醇以及免疫抑制劑，對於治療反應不佳的患者可以考慮採用抗B細胞治療。
主题分类 醫藥衛生 > 基礎醫學
醫藥衛生 > 社會醫學
参考文献
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