認識POEMS症候群

10.6666/ClinMed.201909_84(3).0099

謝秉翰；賴峻毅；龔雅文；蕭樑材

POEMS syndrome（POEMS症候群）

臨床醫學月刊

84卷3期（2019 / 09 / 27）

596 - 605

繁體中文

POEMS症候群主要包含了多發性神經病變（polyneuropathy）、器官腫大（organomegaly）、內分泌疾患（endocrinopathy）、單株免疫球蛋白（monoclonal protein），及皮膚改變（skin changes）等症狀。本文首先藉由臨床案例引導出此疾病的診斷歷程，進一步介紹此疾病臨床上症狀的特徵與細節，診斷標準與治療的進展。最後再藉由此案例檢討臨床上常見的診斷迷思，以期能讓臨床醫師對此疾病更佳熟稔。

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